Text Box: CONGENITAL PORTOHEPATIC SHUNT ASSOCIATED WITH THROMBOCYTOPENIA AND ANEMIA CANTER B1, KOC E1, TURAN O1, YUCEL C2, ERGENEKON E1, ATALAY Y1 1 Gazi University, School of Medicine, Department of Neonatology, Ankara, Turkey 2 Gazi University, School of Medicine, Department of Radiology, Ankara, Turkey Congenital portohepatic shunt is a very rare disorder that is frequently associated with hypergalactosemia, hyperamonemia and encephalopathy. Thrombocytopenia and anemia which may be seen in this pathology are emphasized in animal studies on this issue but underestimated in almost all human studies which usually emphasize the association of this disorder with hypergalactosemia, hyperamonemia and encephalopathy. In this report, we describe a newborn who was referred to our hospital due to his unexplained anemia, thrombocytopenia and hepatosplenomegaly and was found to have congenital portohepatic shunt in the absence of hypergalactosemia, hyperamonemia and encephalopathy. 1900