CONGENITAL HYPOPLASIA OF THE DEPRESSOR ANGULARIS ORIS MUSCLE (CHDAOM)

IS IT JUST ACOSMETIC PROBLEM?

Dr. Mohmmad AA

Islamic Hospital, Amman, Jordan

Islamic.Hospital@index.com.jo or fima@index.com.jo www.islamic-hospital.com.jo

 

Objectives: To emphasize the importance of correct diagnosis, to estimate the incidence & to look for associated problems of CHDAOM, also called Asymmetric Crying Facies.

Method: A prospective study conducted in our pediatric & neonatal department from Jan. 93  Dec. 2000 (over 8 years) looking for signs of mouth deviation to one side during crying, laughing or speech, excluding VII nerve involvement, searching for any minor or major anomalies by performing complete physical & neurological examination. Several variables were studied including the (age, sex, gestational age, mode of delivery, birth weight & the side of the mouth affected).

Results: A total of 24 cases were diagnosed over an 8-year period. The frequency in the neonatal age group is about 0.4/1000 live births. The majority was diagnosed in the early neonatal period (18).

'       Male /Female ratio; 13/11.

'       Mode of delivery: vaginal in 15, vacuum in 5, C.S in 4 cases.

'       Birth weight category: AGA in 16, SGA in 7 & LGA in 1.

'       Full-term in 20 & preterm in 4.

'       Left sided involvement in 19 & right side in 5 !!!

'       Associated congenital heart disease in 1 (ASD); cerebral palsy with brain

atrophy & seizures in 1, Failure to thrive in 1 & minor skin lesion in 1.

'       Positive family history in 1 case.

Conclusion:

1.                       CHDAOM is not rare in children & the best time for its diagnosis is a

careful physical examination of the newborn babies.

2.      It should not be confused with facial nerve palsy.

2.                       It is mainly a cosmetic problem in the majority of cases but it may be

associated with other serious congenital abnormalities.

 
2248