ULTRASHORT HIRSCHSPRUNG’S DISEASE: SURGICAL TREATMENT IN
ASSIUT-EGYPT
Ahmed E. Essa, Mahmoud M. Mostafa
Department of
Pediatric Surgery, Faculty of Medicine, Assiut University, Assiut, Egypt
Objective: To
evaluate the efficacy of using anorectal myectomy technique in the
treatment of ultrashort Hirschsprung’s disease (HD).
Methods: 24
infants and children suffering from chronic constipation and abdominal
distension with or without fecal soiling since birth, admitted to the
pediatric surgical department at Assiut university hospital were included.
Their aged varied from 3 months to 2 years (male 20 and female 4). The
criteria for diagnosis of ultrashort HD were based on barium enema where
dilated rectum was seen and rectal biopsy showed the absence of ganglionic
cells. All cases fulfilled these criteria.
Results: The
clinical improvement of the cases after anorectal myectomy was satisfactory
in all the cases except 4 minor complications in 2 cases. These cases
represent 1/6 of cases of congenital megacolon were treated by the classic
surgical operation at the same period.
Conclusion: Anorectal
myectomuy is a safe, simple, easy procedure and is not associated with
major complications. Also it doesn’t interfere with subsequent pullthrough
ooeration later on if required. It is curative for the properly selected
cases of ultrashort HD.